A mutation that inactivates a specific enzyme (glycogen synt…

A mutation that inactivates a specific enzyme (glycogen synthase) involved in the transfer of a glucosyl residue from UDP-glucose onto a growing glycogen particle is found in a small number of patients. These patients are glycogen deficient, meaning they are unable to store glucose as glycogen.

A person diagnosed with Tarui disease has defective (inactiv…

A person diagnosed with Tarui disease has defective (inactive) PFK-1 (enzyme that catalyzes committed step in glycolysis) in their muscle cells. Which of the following molecules would be the major fuel source (that is could be used to produce ATP) for these cells?