A 6 year old child presents with short stature, polydactyl o…

A 6 year old child presents with short stature, polydactyl of the hands, and a congenital heart defect.  Oral examination reveals the anterior maxillary vestibular sulcus is absent, and several teeth have a conical shape.  Which of the following inherited disorders is the most consistent with these findings? 

A 36 year old patient presents with a well-defined, inverted…

A 36 year old patient presents with a well-defined, inverted pear-shaped radiolucency between the maxillary lateral incisor and canine on a panoramic radiograph.  The roots of the adjacent teeth are diverging.  Which of the following is the most likely diagnosis?